IS Case 304: Cystic fibrosis
Imaging Sciences URMC 2009
Publication Date: 2009-08-06
Cystic fibrosis is a hereditary disease affecting the exocrine glands of the lungs, liver, pancreas, and intestines, causing progressive disability due to multisystem failure. Thick mucus production results in frequent lung infections resulting in bronchiectasis and peribronchial thickening. Thickened secretions from the pancreas can eventually lead to pancreatic atrophy. These features are seen in the presented images.
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